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Image features of atypical teratoid/rhabdoid tumor of central nervous system in children
LI Yanhua  PENG Yun  BAI Jie  WEN Yang  ZHANG Ningning  CHENG Hua  LIU Yue 

Cite this article as: Li YH, Peng Y, Bai J, et al. Image features of atypical teratoid/rhabdoid tumor of central nervous system in children[J]. Chin J Magn Reson Imaging, 2021, 12(10): 49-52, 56. DOI:10.12015/issn.1674-8034.2021.10.011.


[Abstract] Objective To investigate the imaging findings of central nervous system (CNS) atypical teratoid / rhabdoid tumor (AT/RT) in children and to improve the diagnostic level of AT/RT. Materials andMethods The clinical and image data of 9 children with AT/RT were analyzed retrospectively.Results The median age of patients was 19 months, 5 cases were infratentorial, 1 case was supratentorial, 3 cases involved both supratentorial and infratentorial. The maximum diameter of the tumor was 49.9±18.3 mm, 7 cases with peripheral tumor cysts and 6 cases with intratumoral hemorrhage,3 cases with brain metastasis,1 with both brain and spinal cord metastasis. The solid components of the tumor were mainly iso-or high-density on CT, MRI showed mixed intensity on T2WI and high intensity on DWI with low ADC value, the tumor showed various enhancement modes.Conclusion CNS AT/RT of children have some relatively specific imaging findings, which is helpful for diagnosis.
[Keywords] atypical teratoid/rhabdoid tumor;central nervous system;imaging diagnosis;magnetic resonance imaging;apparent diffusion coefficient

LI Yanhua   PENG Yun   BAI Jie   WEN Yang   ZHANG Ningning   CHENG Hua   LIU Yue*  

Imaging Center, Beijing Children's Hospital, Capital Medical University, National Center for Children's Health, Beijing 100045, China

Liu Y, E-mail: liuyue20136@163.com

Conflicts of interest   None.

Received  2021-03-31
Accepted  2021-06-23
DOI: 10.12015/issn.1674-8034.2021.10.011
Cite this article as: Li YH, Peng Y, Bai J, et al. Image features of atypical teratoid/rhabdoid tumor of central nervous system in children[J]. Chin J Magn Reson Imaging, 2021, 12(10): 49-52, 56. DOI:10.12015/issn.1674-8034.2021.10.011.

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